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ACAD8 Antibody

  • 中文名稱:
    ACAD8兔多克隆抗體
  • 貨號(hào):
    CSB-PA892457LA01HU
  • 規(guī)格:
    ¥440
  • 促銷:
    小規(guī)格抗體限時(shí)一口價(jià)
  • 圖片:
    • Western Blot
      Positive WB detected in: Mouse liver tissue, Mouse heart tissue, Mouse skeletal muscle tissue
      All lanes: ACAD8 antibody at 3μg/ml
      Secondary
      Goat polyclonal to rabbit IgG at 1/50000 dilution
      Predicted band size: 46, 32, 39 kDa
      Observed band size: 46, 39 kDa
    • Immunohistochemistry of paraffin-embedded human tonsil tissue using CSB-PA892457LA01HU at dilution of 1:100
  • 其他:

產(chǎn)品詳情

  • 產(chǎn)品名稱:
    Rabbit anti-Homo sapiens (Human) ACAD8 Polyclonal antibody
  • Uniprot No.:
  • 基因名:
    ACAD8
  • 別名:
    ACAD 8 antibody; ACAD-8 antibody; ACAD8 antibody; ACAD8_HUMAN antibody; Activator-recruited cofactor 42 kDa component antibody; Acyl CoA dehydrogenase family member 8 antibody; Acyl Coenzyme A dehydrogenase family member 8 antibody; Acyl-CoA dehydrogenase family member 8 antibody; ARC42 antibody; FLJ22590 antibody; IBD antibody; Isobutyryl-CoA dehydrogenase antibody; Isobutyryl-CoA dehydrogenase; mitochondrial antibody; mitochondrial antibody
  • 宿主:
    Rabbit
  • 反應(yīng)種屬:
    Human, Mouse
  • 免疫原:
    Recombinant Human Isobutyryl-CoA dehydrogenase, mitochondrial protein (201-415AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標(biāo)記方式:
    Non-conjugated

    本頁(yè)面中的產(chǎn)品,ACAD8 Antibody (CSB-PA892457LA01HU),的標(biāo)記方式是Non-conjugated。對(duì)于ACAD8 Antibody,我們還提供其他標(biāo)記。見下表:

    可提供標(biāo)記
    標(biāo)記方式 貨號(hào) 產(chǎn)品名稱 應(yīng)用
    HRP CSB-PA892457LB01HU ACAD8 Antibody, HRP conjugated ELISA
    FITC CSB-PA892457LC01HU ACAD8 Antibody, FITC conjugated
    Biotin CSB-PA892457LD01HU ACAD8 Antibody, Biotin conjugated ELISA
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
  • 產(chǎn)品提供形式:
    Liquid
  • 應(yīng)用范圍:
    ELISA, WB, IHC
  • 推薦稀釋比:
    Application Recommended Dilution
    WB 1:500-1:5000
    IHC 1:20-1:200
  • Protocols:
  • 儲(chǔ)存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.

產(chǎn)品評(píng)價(jià)

靶點(diǎn)詳情

  • 功能:
    Isobutyryl-CoA dehydrogenase which catalyzes one of the steps of the valine catabolic pathway. To a lesser extent, is also able to catalyze the oxidation of (2S)-2-methylbutanoyl-CoA.
  • 基因功能參考文獻(xiàn):
    1. we discovered a novel c.1156_1158delCAG mutation in ACAD8 in patients with isobutyryl-CoA dehydrogenase deficiency , and investigated the mutation spectrum of ACAD8. PMID: 24635911
    2. first enzymatic and molecular confirmation of a deficiency of this enzyme in a patient PMID: 12359132
  • 相關(guān)疾?。?/div>
    Isobutyryl-CoA dehydrogenase deficiency (IBDD)
  • 亞細(xì)胞定位:
    Mitochondrion.
  • 蛋白家族:
    Acyl-CoA dehydrogenase family
  • 組織特異性:
    Detected at comparable levels in all tissues examined (heart, lung, brain, skeletal muscle, pancreas and placenta). Weakly expressed in liver and kidney.
  • 數(shù)據(jù)庫(kù)鏈接:

    HGNC: 87

    OMIM: 604773

    KEGG: hsa:27034

    STRING: 9606.ENSP00000281182

    UniGene: Hs.14791